منابع مشابه
Congenital pulmonary lymphangiectasia
Congenital pulmonary lymphangiectasia (PL) is a rare developmental disorder involving the lung, and characterized by pulmonary subpleural, interlobar, perivascular and peribronchial lymphatic dilatation. The prevalence is unknown. PL presents at birth with severe respiratory distress, tachypnea and cyanosis, with a very high mortality rate at or within a few hours of birth. Most reported cases ...
متن کاملPrimary pulmonary lymphangiectasia in infancy and childhood.
Primary pulmonary lymphangiectasia (PPL) is a rare disorder of unknown aetiology characterised by dilatation of the pulmonary lymphatics. PPL is widely reported to have a poor prognosis in the neonatal period and little is known about the clinical features of patients who survive the newborn period. The current authors report the outcome in nine patients diagnosed in infancy with PPL over a 15-...
متن کاملCongenital Pulmonary Lymphangiectasia, Associated with Total Anomalous Pulmonary Venous Return
Congenital pulmonary lymphangiectasia (CPL) is a rare pathological diagnosis. It was first reported by Virchow in 1856. CPL is histologically characterized by pulmonary lymphatic dilatation without lymphatic proliferation in the subpleural, peribronchovascular and interlobular areas. The prognosis of CPL is very poor where approximately 50% of all infants are stillborn and most others usually d...
متن کاملPneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ven...
متن کاملIntestinal Lymphangiectasia
History A three year old boy presented with tetanus who additionally suffered from nonbloody diarrhea. Physical examination showed bilateral edema of the lower limbs. Laboratory data showed iron deficiency anemia, hypoalbuminemia, hypocalcaemia and hypogammaglobulinemia. Stool culture was negative for bacteria however fat droplets were detected in the patient’s stool. Endoscopic examination rev...
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ژورنال
عنوان ژورنال: American Journal of Roentgenology
سال: 1972
ISSN: 0361-803X,1546-3141
DOI: 10.2214/ajr.116.3.548